PAPERS - RESEARCH FRONT: 15

TITLE 1ST AUTHOR YEAR
PRION DISEASE - SPONGIFORM ENCEPHALOPATHIES UNVEILED null 1990
AMINO-ACID POLYMORPHISM IN HUMAN PRION PROTEIN AND AGE AT DEATH IN INHERITED PRION DISEASE BAKER HF 1991
AMYLOID FILAMENTS IN INCLUSION BODY MYOSITIS - NOVEL FINDINGS PROVIDE INSIGHT INTO NATURE OF FILAMENTS MENDELL JR 1991
FATAL FAMILIAL INSOMNIA, A PRION DISEASE WITH A MUTATION AT CODON-178 OF THE PRION PROTEIN GENE MEDORI R 1992
PRION DISEASE JOHNSON RT 1992
INHERITED PRION DISEASE WITH 144 BASE PAIR GENE INSERTION .1. GENEALOGICAL AND MOLECULAR STUDIES POULTER M 1992
INHERITED PRION DISEASE WITH 144 BASE PAIR GENE INSERTION .2. CLINICAL AND PATHOLOGICAL FEATURES COLLINGE J 1992
SPONTANEOUS CONVERSION OF PRP(C) TO PRP(SC) SULKOWSKI E 1992
INHERITED PRION DISEASE (PRP LYSINE-200) IN BRITAIN - 2 CASE-REPORTS COLLINGE J 1993
PRION DISEASES IN HUMANS AND THEIR RELEVANCE TO OTHER NEURODEGENERATIVE DISEASES COLLINGE J 1993
DEMENTIA ASSOCIATED WITH A 216 BASE-PAIR INSERTION IN THE PRION PROTEIN GENE - CLINICAL AND NEUROPATHOLOGICAL FEATURES DUCHEN LW 1993
CEREBRAL AMYLOID IN HUMAN PRION DISEASE WATANABE R 1993
EVIDENCE FOR THE EXPERIMENTAL TRANSMISSION OF CEREBRAL BETA-AMYLOIDOSIS TO PRIMATES BAKER HF 1993
A NEW INHERITED PRION DISEASE (PRP-P105L MUTATION) SHOWING SPASTIC PARAPARESIS KITAMOTO T 1993
THE GENETICS AND TRANSGENETICS OF HUMAN PRION DISEASE HSIAO KK 1994
INDUCTION OF BETA(A4)-AMYLOID IN PRIMATES BY INJECTION OF ALZHEIMERS-DISEASE BRAIN HOMOGENATE - COMPARISON WITH TRANSMISSION OF SPONGIFORM ENCEPHALOPATHY BAKER HF 1994
MOLECULAR-GENETICS OF HUMAN PRION DISEASES COLLINGE J 1994
DEFINING THE LIMITS OF PRION DISEASE RIDLEY RM 1994
PERCEPTIONS OF PRION DISEASE RIDLEY RM 1994
DIRECT SEQUENCING OF PCR AMPLIFIED PIG PRP GENES MARTIN T 1995
PRION DISEASE WITH 144-BASE-PAIR INSERTION IN A JAPANESE FAMILY LINE ODA T 1995
COMPLETE PENETRANCE OF CREUTZFELDT-JAKOB-DISEASE IN LIBYAN JEWS CARRYING THE E200K MUTATION IN THE PRION PROTEIN GENE SPUDICH S 1995
PRION DISEASE (PRP-A117V) PRESENTING WITH ATAXIA INSTEAD OF DEMENTIA MASTRIANNI JA 1995
Hypokinesia and presenile dementia in a Dutch family with a novel insertion in the prion protein gene vanGool WA 1995
PRION DISEASE-ASSOCIATED WITH A NOVEL 9 OCTAPEPTIDE REPEAT INSERTION IN THE PRNP GENE KRASEMANN S 1995
Human prion disease and human prion protein disease Kitamoto T 1996
Insoluble wild-type and protease-resistant mutant prion protein in brains of patients with inherited prion disease Gabizon R 1996
A prion disease with a novel 96-base pair insertional mutation in the prion protein gene Campbell TA 1996
Mutation of the prion protein gene at codon 208 in familial Creutzfeldt-Jakob disease Mastrianni JA 1996
The evolution of views on the nosological position of transmissible spongiform encephalopathies Liberski PP 1997
Neuropsychiatric presentations of prion disease Mallucci GR 1997
Familial Creutzfeldt-Jakob disease - Codon 200 prion disease in Libyan Jews Meiner Z 1997
Familial prion disease with a novel 144-bp insertion in the prion protein gene in a Basque family Capellari S 1997
The prion diseases: Creutzfeldt-Jakob, Gerstmann-Straussler-Scheinker, and related disorders Mastrianni JA 1998
An inherited prion disease with a PrPP105L mutation - Clinicopathologic and PrP heterogeneity Yamada M 1999
Inherited prion disease with an alanine to valine mutation at codon 117 in the prion protein gene Mallucci GR 1999
Gerstmann-Straussler-Scheinker disease - The dilemma of molecular and clinical correlations Boellaard JW 1999
Prominent psychiatric features and early onset in an inherited prion disease with a new insertional mutation in the prion protein gene Laplanche JL 1999
Prion protein with an E200K mutation displays properties similar to those of the cellular isoform PrPC Rosenmann H 2001
Hereditary Creutzfeldt-Jakob disease and fatal familial insomnia Gambetti P 2003